Glutaryl-L-carnitine lithium salt is a specialized biochemical reagent used primarily in research on acylcarnitine metabolism and organic acid disorders, such as glutaric aciduria type I. It serves as a key marker for the accumulation of glutaryl-CoA conjugates due to deficiencies in enzymes like glutaryl-CoA dehydrogenase. This compound is employed in studies investigating mitochondrial fatty acid and amino acid catabolism pathways, including the role of carnitine in acyl group transport and detoxification. It is also utilized as an intermediate in the laboratory synthesis of related biochemicals and in developing diagnostic assays or therapeutic strategies for metabolic dysfunctions, providing insights into energy metabolism and potential treatments for related neurodegenerative conditions.